Jornal do Sistema Genital e Distúrbios

Obstructed Hemivagina with Ipsilateral Renal Anomaly(OHVIRA) Syndrome - A Rare Congenital Anomaly

Thejaswini Jaiprakash, Rajiv Kumar Saxena and Pramila Pandey

Obstructed Hemivagina with Ipsilateral Renal Anomaly(OHVIRA) Syndrome - A Rare Congenital Anomaly

Objective: We present a rare case of Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome with a single septate uterus. This syndrome is shrouded in controversies concerning its nomenclature and development. We attempt to highlight the different viewpoints surrounding this unusual condition, which can be quite distressing for the affected young girls and confusing the treating doctors.