Revista de Pesquisa em Dermatologia Clínica

Papillon Lefevre Syndrome with Hepatic Abscess

Kartal D, Cinar SL, Ferahbas A, Borlu M and Uksal U

Papillon Lefe’vre Syndrome with Hepatic Abscess

PLS is a rare condition with an incidence of between one and four persons per million. The disease is an autosomal recessive inheritance and presents with palmoplantar keratoderma and destructive periodontitis usually beginning in early childhood.