Jornal de Coluna e Neurocirurgia

Proximal-Type Epithelioid Sarcoma: Report of Two Cases with Unusual Location and Review of the Literature

Antonio Nardone, Giulio Anichini, Federico Caporlingua, Manila Antonelli, Gennaro Lapadula, Antonio Santoro and Maurizio Salvati

Proximal-Type Epithelioid Sarcoma: Report of Two Cases with Unusual Location and Review of the Literature

Epithelioid sarcoma usually occurs at the distal extremities of young adults. The proximal-type variant is characterized by a more aggressive course and resistance to treatment. We report two extremely rare cases with unique sites of origin. Due to anatomical issues, in both cases, a one-piece resection was not performed. Both presented a local relapse without any metastasis. Given the rarity of the disease, every report is fundamental for a future characterization of its features.